Класифікація васкулітних захворювань

Category

Disorders

Large-vessel vasculitis

Takayasu arteritis

Giant cell arteritis

Medium-vessel vasculitis

Polyarteritis nodosa

Kawasaki disease

Small-vessel vasculitis

Antineutrophil cytoplasmic antibody (ANCA)–associated vasculitis (AAV)

Immune complex small vessel vasculitis

Variable-vessel vasculitis

Behçet's disease

Cogan syndrome

Single-organ vasculitis

Cutaneous small vessel vasculitis

Primary central nervous system vasculitis

Isolated aortitis

Data from Jennette JC, Falk RJ, Bacon PA, et al. 2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides. Arthritis Rheum 2013;65(1):1-11. doi:10.1002/art.37715