Класифікація васкулітних захворювань

Size of Predominant Affected Vessels

Disorders

Symptoms and Signs

Large

Behçet disease

Giant cell arteritis

Takayasu arteritis

Limb claudication

Unequal blood pressure measurements or unequal pulse strength/absent pulse in the limbs

Central nervous system and retinal ischemic symptoms (eg, strokes)

Medium

Medium-vessel cutaneous vasculitis

Polyarteritis nodosa

Kawasaki disease

Symptoms of tissue infarction in affected organs, such as

  • Muscles: Myalgias

  • Nerves: Numbness, paresthesias, and/or weakness. Multiple mononeuropathy (mononeuritis multiplex) or polyneuropathy

  • Gastrointestinal tract: Abdominal pain, weight loss, and/or diarrhea. Mesenteric ischemia

  • Kidneys: New-onset hypertension (with renal artery involvement)

  • Skin: Ulcers, nodules, and livedo reticularis

Symptoms and signs in Kawasaki disease: Fever, rash, lymphadenopathy, conjunctivitis, and coronary artery aneurysms

Small

Eosinophilic granulomatosis with polyangiitis

Cryoglobulinemic vasculitis

Granulomatosis with polyangiitis

Immunoglobulin A–associated vasculitis (formerly called Henoch-Schönlein purpura)

Microscopic polyangiitis

Small-vessel cutaneous vasculitis

Symptoms of tissue infarction in affected organs similar to those for medium-sized vessels, except skin lesions more likely to be purpuric

In kidneys: Glomerulonephritis (usually asymptomatic)