Conditions Associated With Multiple Endocrine Neoplasia Syndromes

Hyperparathyroidism

≥ 95%

10–20%

—

55–80%

Enteropancreatic tumors

30–80%

—

—

15–25%

Pituitary adenomas

15–42%

—

—

30–45%

Medullary thyroid carcinoma

—

> 95%

> 95%

—

Pheochromocytomas

—

40–50%

50%

—

Adrenal cortex tumors

33%

—

—

—

Mucosal neuromas

—

—

≈ 100%

—

Marfanoid habitus

—

—

≈ 100%

—

Neuroendocrine tumors

10–15%

—

—

5%

Lipomas

up to 35%

—

—

—

Angioma or collagenomas (especially on the face)

70–85%

—

—

—