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Prion Disease Associated With Diarrhea and Autonomic Neuropathy

(Prion Protein Systemic Amyloidosis)

By

Brian Appleby

, MD, Case Western Reserve University

Medically Reviewed Nov 2022
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Prion disease associated with diarrhea and autonomic neuropathy is a prion disease that initially affects nerves outside the brain, causing diarrhea and loss of feeling in the feet.

Prion disease associated with diarrhea and autonomic neuropathy differs from other prion diseases as follows:

The disease progresses over decades. People may live up to 30 years after symptoms develop.

There is no cure at present. Treatment focuses on relieving symptoms.

NOTE: This is the Consumer Version. DOCTORS: VIEW PROFESSIONAL VERSION
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