Primary Lymphedemas

Primary Lymphedemas

Disorder

Age at Symptom Onset

Comments

Congenital lymphedema

Before age 2 years

In Milroy disease, a subtype, the toenails are often abnormal. Male infants may have swelling in the scrotum, called a hydrocele. Sometimes diarrhea and jaundice (yellowing of the skin and whites of the eyes) occur.

Lymphedema praecox

2–35 years

Also called Meige disease. Typically occurs in females at the onset of menses. Usually the swelling is painless and can affect one or both legs.

Lymphedema tarda

After age 35 years

Some (but not all) affected people may have family members with this disorder.

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